Incidence
- age <30; no sex predilection
Location
- mandible, femur, pelvic bones, radius, and tibia
Clinical Features
- Tooth mobility, proptosis, concurrent infection, and dysesthesia are reported infrequently.
- If the lesion erodes through the cortex, then an accompanying soft tissue mass will be present. When this occurs, it may be difficult to determine whether the lesion is a desmoplastic fibroma of bone with soft tissue extension or a soft tissue fibromatosis with secondary extension into bone.
- Adjacent teeth may exhibit displacement and root resorption.
Radiographic Features
- multilocular or occasionally unilocular radiolucent lesion; well-defined or ill-defined margins
Compare to
- osseous counterpart of soft tissue fibromatosis (desmoid tumor)
Treatment
- Curettage may be adequate for localized lesions without cortical perforation or soft tissue extension, but segmental resection is preferred for lesions exhibiting rapid growth, an ill-defined radiographic appearance, cortical perforation, or soft tissue extension
